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Cholestasis
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Definition
: Impairment of bile flow due to obstruction in small bile ducts (INTRAHEPATIC CHOLESTASIS) or obstruction in large bile ducts (EXTRAHEPATIC CHOLESTASIS).
See Also
Jaundice, Obstructive
Examples
Cholestasis, Extrahepatic
;
Cholestasis, Intrahepatic
;
Mirizzi Syndrome
Other names
Biliary Stasis; Bile Duct Obstruction; Stases, Biliary; Obstructions, Bile Duct; Obstruction, Bile Duct; Duct Obstructions, Bile; Duct Obstruction, Bile; Cholestases; Biliary Stases; Bile Duct Obstructions; Stasis, Biliary
Substance
CAS Registry & name
Categories
Source
Finnish lethal neonatal metabolic syndrome
0
*Acidosis, Lactic
*Renal Aminoacidurias
*Cholestasis
*Fetal Growth Retardation
*Hemosiderosis
*Metabolism, Inborn Errors.
Lutz Richner Landolt syndrome
0
*Abnormalities, Multiple
*Cholestasis
*Jaundice
*Renal Insufficiency.
COACH syndrome
0
*Abnormalities, Multiple
*Ataxia
*Cholestasis
*Coloboma
*Liver Diseases
Brain/abnormalities.
Cholesterol pneumonia
0
*Cholestasis
*Pneumonia.
Hardikar syndrome
0
*Cholestasis
*Cleft Palate
*Retinitis Pigmentosa.
Bile acid synthesis defect, congenital, 2
0
*Cholestasis
*Metabolism, Inborn Errors
Oxidoreductases/deficiency.
Bile acid synthesis defect, congenital, 1
0
*Cholestasis
*Metabolism, Inborn Errors.
Arthrogryposis renal dysfunction cholestasis syndrome
0
*Arthrogryposis
*Cholestasis
*Renal Insufficiency.
Aagenaes syndrome
0
*Cholestasis
*Lymphedema.