Definition: Chronic form of ichthyosis that is inherited as a sex-linked recessive trait carried on the X-chromosome and transmitted to the male offspring. It is characterized by severe scaling, especially on the extremities, and is associated with steroid sulfatase deficiency.
do not use /congen & do not coord with INFANT, NEWBORN, DISEASES
See AlsoSteryl-Sulfatase
Other names Steroid Sulfatase Deficiency Disease; Ichthyosis, Sex-Linked; Ichthyosis, X Linked; Ichthyosis, Sex Linked; Ichthyoses, X-Linked; Ichthyoses, Sex-Linked; Steroid Sulfatase Deficiency; Placental Steroid Sulfatase Deficiency
