Definition: A heritable disorder of faulty keratinization characterized by the proliferation of abnormal clones of KERATINOCYTES and lesions showing varying atrophic patches surrounded by an elevated, keratotic border. These keratotic lesions can progress to overt cutaneous neoplasm. Several clinical variants are recognized, including porokeratosis of Mibelli, linear porokeratosis, disseminated superficial actinic porokeratosis, palmoplantar porokeratosis, and punctate porokeratosis.
do not confuse with PARAKERATOSIS
Other names Porokeratosis, Punctate; Porokeratosis, Palmoplantar; Porokeratosis, Mibelli; Porokeratosis, Linear; Porokeratosis, Disseminated Superficial Actinic; Porokeratosis of Mibelli; Porokeratosis Palmaris et Plantaris Disseminata; Punctate Porokeratosis; Palmoplantar Porokeratosis; Mibelli Porokeratosis; Linear Porokeratosis; Type 2 Punctate PPK; Porokeratosis, Disseminated Superficial Actinic 2; Porokeratosis Plantaris Palmaris et Disseminata; Keratoderma Palmoplantar, Punctate Type 2; Disseminated Superficial Actinic Porokeratosis