Definition: A flavoprotein enzyme that is responsible for the catabolism of LYSINE; HYDROXYLYSINE; and TRYPTOPHAN. It catalyzes the oxidation of GLUTARYL-CoA to crotonoyl-CoA using FAD as a cofactor. Glutaric aciduria type I is an inborn error of metabolism due to the deficiency of glutaryl-CoA dehydrogenase.
Other names Dehydrogenase, Glutaryl-Coenzyme A; Dehydrogenase, Glutaryl-CoA; Dehydrogenase, Glutaryl CoA; CoA Dehydrogenase, Glutaryl; Glutaryl-Coenzyme A Dehydrogenase; Glutaryl CoA Dehydrogenase; Glutaryl Coenzyme A Dehydrogenase
