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Velaglucerase alfa, human
under Glucosylceramidase
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Glucosylceramidase
Definition
: A glycosidase that hydrolyzes a glucosylceramide to yield free ceramide plus glucose. Deficiency of this enzyme leads to abnormally high concentrations of glucosylceramide in the brain in GAUCHER DISEASE. EC 3.2.1.45.
/defic: consider also GAUCHER DISEASE
Other names
Glucocerebrosidase; beta-
Glucosidase, Glucosylceramide; beta-
Glucosidase, Glucocerebroside; beta-
Glucosidase, Acid; beta Glucocerebrosidase; Hydrolase, Glucosylsphingosine Glucosyl; Glucosylceramide beta Glucosidase; Glucosyl Hydrolase, Glucosylsphingosine; Glucocerebroside beta Glucosidase; Ceramidase, Glucosyl; Acid beta Glucosidase; beta-
Glucocerebrosidase; Glucosylsphingosine Glucosyl Hydrolase; Glucosylceramide beta-
Glucosidase; Glucosyl Ceramidase; Glucocerebroside beta-
Glucosidase; Acid beta-
Glucosidase
Drugs:
ELELYSO
Substance
CAS Registry & name
Categories
Source
Drugs
*
Velaglucerase alfa, human
a human recombinant glucocerebrosidase enzyme replacement therapy for type 1 Gaucher disease
EC 3.2.1.45
*Glucosylceramidase
Curr Opin Investig Drugs. 2010 Apr;11(4):472-8
VPRIV