Definition: A familial coagulation disorder characterized by a prolonged bleeding time, unusually large platelets, and impaired prothrombin consumption.
Other names Syndromes, Giant Platelet; Syndrome, Giant Platelet; Syndrome, Bernard-Soulier; Platelet Syndromes, Giant; Bernard Soulier Syndrome; Von Willebrand Factor Receptor Deficiency; Platelet Glycoprotein 1b, Deficiency of; Deficiency of Platelet Glycoprotein 1b; Giant Platelet Syndrome