Definition: A hypertriglyceridemia disorder, often with autosomal dominant inheritance. It is characterized by the persistent elevations of plasma TRIGLYCERIDES, endogenously synthesized and contained predominantly in VERY-LOW-DENSITY LIPOPROTEINS (pre-beta lipoproteins). In contrast, the plasma CHOLESTEROL and PHOSPHOLIPIDS usually remain within normal limits.
Other names Hypertriglyceridemia, Familial; Hyperprebetalipoproteinemia; Type IV, Hyperlipoproteinemia; Familial Hypertriglyceridemia; Hyper prebeta lipoproteinemia
