Hemophilia B (definition)

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Hemophilia B

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Definition: A deficiency of blood coagulation factor IX inherited as an X-linked disorder. (Also known as Christmas Disease, after the first patient studied in detail, not the holy day.) Historical and clinical features resemble those in classic hemophilia (HEMOPHILIA A), but patients present with fewer symptoms. Severity of bleeding is usually similar in members of a single family. Many patients are asymptomatic until the hemostatic system is stressed by surgery or trauma. Treatment is similar to that for hemophilia A. (From Cecil Textbook of Medicine, 19th ed, p1008)

See Also Hemophilia A

Other names Factor IX Deficiency; Christmas Disease; Hemophilia Bs; Haemophilia Bs; Factor IX Deficiencies; Disease, Christmas; Deficiencies, Factor IX; Bs, Hemophilia; Bs, Haemophilia; B, Hemophilia; B, Haemophilia; Haemophilia B; Deficiency, Factor IX

Substance	CAS Registry & name	Categories	Source
factor IX Seattle(2)	0	*Factor IX Hemophilia B.	J Clin Invest 1987;80(4):1023
factor IX Chapel Hill	68993-76-0 Blood-coagulation factor IX Chapel Hill	*Factor IX Hemophilia B.	Proc Natl Acad Sci USA 1983;80(14):4200

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Sources: NLM Medical Subject Headings, NIH UMLS, Drugs@FDA, FDA AERS original data copyright United States Government. No endorsement implied. Last modified 6/6/2012
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