Definition: An enzyme that catalyzes the conversion of methylmalonyl-CoA to succinyl-CoA by transfer of the carbonyl group. It requires a cobamide coenzyme. A block in this enzymatic conversion leads to the metabolic disease, methylmalonic aciduria. EC 5.4.99.2.
Other names Methylmalonyl-CoA Isomerase; Mutase, Methylmalonyl-CoA; Methylmalonyl CoA Mutase; Methylmalonyl CoA Isomerase; Isomerase, Methylmalonyl-CoA