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Pyroglutamate Hydrolase
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Definition
: Hydrolyzes pyroglutamic acid in the presence of ATP to glutamate plus ADP and inorganic phosphate. Deficiency leads to pyroglutamic acidurea.
Other names
Hydrolase, Pyroglutamate; 5 Oxoprolinase; 5-
Oxoprolinase; Oxoprolinase
Substance
CAS Registry & name
Categories
Source
Drugs
*
2-
imidazolidone-
4-
carboxylic acid
0
*Imidazolines
Pyroglutamate Hydrolase/antagonists & inhibitors.
Proc Natl Acad Sci U S A 1973 Mar;70(3):759-61
5-
oxoprolinase deficiency
0
*Amino Acid Metabolism, Inborn Errors
Pyroglutamate Hydrolase/deficiency.