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Pyruvate Dehydrogenase (Lipoamide)
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Definition
: The E1 component of the multienzyme PYRUVATE DEHYDROGENASE COMPLEX. It is composed of 2 alpha subunits (pyruvate dehydrogenase E1 alpha subunit) and 2 beta subunits (pyruvate dehydrogenase E1 beta subunit).
Other names
Pyruvate Dehydrogenase E1; Pyruvate Dehydrogenase-
E1; Pyruvate Dehydrogenase Component E1; Pyruvate Decarboxylase (Lipoamide)
Substance
CAS Registry & name
Categories
Source
Drugs
*
PDHA2 protein, human
EC 1.2.4.1
*Pyruvate Dehydrogenase (Lipoamide).
Mol Genet Metab. 2010 Apr;99(4):425-30
pyruvate dehydrogenase E1 beta subunit
EC 1.2.4.1
*Pyruvate Dehydrogenase (Lipoamide).
J Bacteriol 1998 Mar;180(6):1540-8
pyruvate dehydrogenase E1alpha subunit
EC 1.2.4.1
*Pyruvate Dehydrogenase (Lipoamide)
Leigh Disease.
Nucleic Acids Res 1990;18(16):4925