Definition: A PYRIDOXAL PHOSPHATE dependent enzyme that catalyzes the decarboxylation of GLYCINE with the transfer of an aminomethyl group to the LIPOIC ACID moiety of the GLYCINE DECARBOXYLASE COMPLEX H-PROTEIN. Defects in P-protein are the cause of non-ketotic hyperglycinemia. It is one of four subunits of the glycine decarboxylase complex.
Other names P protein, Glycine Decarboxylase; Glycine Decarboxylase P-protein; Glycine Decarboxylase Complex P Protein; Glycine Cleavage System P Protein; Decarboxylase, Glycine; Decarboxylase P-protein, Glycine; P-protein, Glycine Decarboxylase; Glycine Decarboxylase Complex P-Protein; Glycine Decarboxylase; Glycine Cleavage System P-Protein
