Definition: A LIVER mitochondrial matrix flavoenzyme that catalyzes the oxidation of SARCOSINE to GLYCINE and FORMALDEHYDE. Mutation in the enzyme causes sarcosinemia, a rare autosomal metabolic defect characterized by elevated levels of SARCOSINE in BLOOD and URINE.
Other names Sarcosine N Demethylase; N-Demethylase, Sarcosine; Dehydrogenase, Sarcosine; Dehydrogenase, Monomethylglycine; Sarcosine N-Demethylase; Monomethylglycine Dehydrogenase
