Definition: Abnormal thoracoabdominal VISCERA arrangement (visceral heterotaxy) or malformation that involves additional CONGENITAL HEART DEFECTS (e.g., heart isomerism; DEXTROCARDIA) and/or abnormal SPLEEN (e.g., asplenia and polysplenia). Irregularities with the central nervous system, the skeleton and urinary tract are often associated with the syndrome.
Other names Viscerums, Situs Ambiguus; Viscerum, Situs Ambiguus; Visceral Heterotaxies; Syndromes, Polysplenia; Syndromes, Heterotaxy; Syndromes, Asplenia; Syndrome, Polysplenia; Syndrome, Ivemark; Syndrome, Heterotaxy; Syndrome, Asplenia; Situs Ambiguus Viscerums; Right Atrial Isomerisms; Polysplenia Syndromes; Left Atrial Isomerisms; Isomerisms, Right Atrial; Isomerisms, Left Atrial; Isomerism, Right Atrial; Isomerism, Left Atrial; Heterotaxy, Visceral; Heterotaxy Syndromes
