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ψ
Iduronidase
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Definition
: An enzyme that hydrolyzes iduronosidic linkages in desulfated dermatan. Deficiency of this enzyme produces Hurler's syndrome. EC 3.2.1.76.
/defic: consider also MUCOPOLYSACCHARIDOSIS I
See Also
Mucopolysaccharidosis I
Other names
alpha L Iduronidase; alpha L Idosiduronase; alpha-
L-
Iduronidase; alpha-
L-
Idosiduronase
Drugs
*
:
ALDURAZYME
Substance
CAS Registry & name
Categories
Source
Drugs
*
AGT-
181
0
*Antibodies, Monoclonal
*Iduronidase
*Recombinant Fusion Proteins.
J Biotechnol. 2009 Oct 26;144(2):135-41
2-
carboxy-
3,4,5-
trihydroxypiperidine
0
*Pipecolic Acids
Glucuronidase/antagonists & inhibitors
Iduronidase/antagonists & inhibitors.
FEBS Lett 1984;176(1):61