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4-Hydroxyphenylpyruvate Dioxygenase
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Definition
: An enzyme that catalyzes the conversion of 4-hydroxyphenylpyruvate plus oxygen to homogentisic acid and carbon dioxide. EC 1.13.11.27.
/defic: consider also TYROSINE /blood (IM) + AMINO ACID METABOLISM, INBORN ERRORS (IM)
Other names
para-
Hydroxyphenylpyruvate Oxidase; para-
Hydroxyphenylpyruvate Hydroxylase; P-
Hydroxyphenylpyruvate Oxidase; P-
Hydroxyphenylpyruvate Hydroxylase; para Hydroxyphenylpyruvate Oxidase; para Hydroxyphenylpyruvate Hydroxylase; P Hydroxyphenylpyruvate Oxidase; P Hydroxyphenylpyruvate Hydroxylase; Oxidase, para-
Hydroxyphenylpyruvate; Oxidase, P-
Hydroxyphenylpyruvate; Hydroxylase, para-
Hydroxyphenylpyruvate; Hydroxylase, P-
Hydroxyphenylpyruvate; Dioxygenase, 4-
Hydroxyphenylpyruvate
Substance
CAS Registry & name
Categories
Source
Drugs
*
diketonitrile
0
*Nitriles
*Sulfones
4-Hydroxyphenylpyruvate Dioxygenase/antagonists & inhibitors.
Drug News Perspect 2003 Oct;16(8):493-6
3-
fluoro-
3-
(4-
nitrophenyl)pyruvic acid
0
*Phenylpyruvic Acids
4-Hydroxyphenylpyruvate Dioxygenase/antagonists & inhibitors.
Bioorg Med Chem Lett 1999 Jul;7(7):1459-65
3-
fluoro-
3-
phenylpyruvic acid
0
*Phenylpyruvic Acids
4-Hydroxyphenylpyruvate Dioxygenase/antagonists & inhibitors.
/antagonists & inhibitors Bioorg Med Chem Lett 1999 Jul;7(7):1459-65
sulcotrione
99105-77-8
*Cyclohexanones
*Mesylates
4-Hydroxyphenylpyruvate Dioxygenase/antagonists & inhibitors.
FEBS Lett 1993 Mar 1;318(2):162-6
nitisinone
104206-65-7
*Cyclohexanones
*Nitrobenzoates
4-Hydroxyphenylpyruvate Dioxygenase/antagonists & inhibitors.
Pharma Action
Enzyme Inhibitors
Lancet 1992 Oct 3;340(8823):813-7
ORFADIN